Sturge Weber Syndrome-MRI

MRI reveals a pial, enhancing, angiomatous malformation, often in the occipital or posterior temporoparietal region ipsilateral to the facial angioma. Gadolinium enhancement improves visualization of the angiomatous malformation.

Reported by Teleradiology Providers

Sturge Weber Syndrome With Arachnoid Cyst-CT

Sturge-Weber syndrome is one of the neurocutaneous syndromes. It is a rare, nonfamiliar disease that is characterized by facial port-wine stain, leptomeningeal angiomatosis, choroidal angioma, buphthalmos, intracranial calcification, cerebral atrophy, mental retardation, glaucoma, seizures and hemiparesis.

This is 3-year-old boy who had seizures with CT findings consistent with Sturge-Weber syndrome who had in addition temporal arachnoid cyst which is an uncommonly reported association.